Purpose of review:
Although osteofibrous dysplasia and adamantinoma are rare tumors, they occur in sufficient numbers to be encountered by most orthopaedic surgeons. They have similar presentations and are probably histopathologically related. Osteofibrous dysplasia is usually best observed and not operated on, but adamantinoma is a malignancy and should be widely excised.
Recent evaluations have continued to confirm that osteofibrous dysplasia and fibrous dysplasia are distinct, unrelated conditions. Osteofibrous dysplasia is now recognized to be associated with adamantinoma, and there is growing evidence that they are closely related entities.
Osteofibrous dysplasia and adamantinoma are similar and related but are treated much differently. The clinician needs to know how to distinguish between them.
Current Opinion in Orthopedics. 15(6):452-455, December 2004.